Weber-Christian Disease (Clinical Case Description)

T.V. Parakhina, U.I. Pryimych

Abstract


Pfeifer-Weber-Christian disease — a rare autoimmune disease with lesions of subcutaneous adipose tissue. Diagnosis and treatment of this rare type of panniсulitis remain unresolved and will be discussed in this article. Description of a clinical case: the article presents a case of Weber-Christian syndrome in a 53-year-old female patient, who suffered from this disease since she was 17 years old, but during life she has been treated for recurrent thrombophlebitis and erythema nodosum. The final diagnosis is established only at the age of 53 years.


Keywords


autoimmune disease; Pfeifer-Weber-Christian disease; panniсulitis

References


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DOI: https://doi.org/10.22141/2224-1507.3.23.2016.85011

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